Coexistence of TEMPI syndrome and leukocytoclastic vasculitis successfully treated with autologous stem cell transplantation

Coexistence of TEMPI syndrome and leukocytoclastic vasculitis successfully treated with autologous stem cell transplantation

Blog Article

Abstract The TEMPI syndrome is a very rare paraneoplastic syndrome associated with 844 plasma cell dyscrasia and monoclonal gammopathy.First described in 2011, the pathophysiology of TEMPI syndrome is still unknown.Essential for diagnosis is to recognize the five clinical findings: telangiectasias, erythrocytosis IC Hardware and elevated serum erythropoietin, monoclonal gammopathy, perinephric fluid collection, and intrapulmonary shunting.

Here we report a case of a woman with the coexistence of TEMPI and leukocytoclastic vasculitis, shedding light on a possible common inflammatory pathway involved in the pathogenesis of the syndrome.